Description
Interstisial Lung disease
also known Diffuse Parenchymal Lung Disease
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Clubbing
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Reduced chest expansion
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Fine end-inspiratory crackles
at lower zones (basal)
Idiopathic
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Idiopathic pulmonary fibrosis
Secondary
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Connective tissue diseases:
RA, sarcoidosis, SLE,
systemic sclerosis,
dermatomyositis
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Inhaled substances
(pneumoconiosis):
asbestosis, silicosis
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Drugs like nitrofurantoin
and cigarette smoking
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Extrinsic allergic alveolitis
(hypersensitivity pneumonitis)
due to exposure to birds
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Usual interstitial pneumonia
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Asbestosis
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Connective tissue disease
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Basic profile:
CRP, ANA, ANCA, RF
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Stop smoking
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Nicotine replacement therapy
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NAC
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Steroid if inflammatory
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Antifibrotic agent
like pirfenidone
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