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Case Details

Interstisial Lung disease

  • Author: Dr. Hasan Altarrah
  • Published Date: 13/05/2026
  • Last Modified Date:
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  • Category :Internal Medicine
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Additional Information:

  • CC: SOB OR COUGH

Description

Interstisial Lung disease also known Diffuse Parenchymal Lung Disease

Clinical Signs
  • Clubbing
  • Reduced chest expansion
  • Fine end-inspiratory crackles at lower zones (basal)
Causes of ILD

Idiopathic

  • Idiopathic pulmonary fibrosis

Secondary

  • Connective tissue diseases: RA, sarcoidosis, SLE, systemic sclerosis, dermatomyositis
  • Inhaled substances (pneumoconiosis): asbestosis, silicosis
  • Drugs like nitrofurantoin and cigarette smoking
  • Extrinsic allergic alveolitis (hypersensitivity pneumonitis) due to exposure to birds
Causes of Basal Fibrosis
  • Usual interstitial pneumonia
  • Asbestosis
  • Connective tissue disease
What Will You Do?
  • CXR
  • ABG
  • Basic profile: CRP, ANA, ANCA, RF
Management of Pulmonary Fibrosis
Non Pharmacological
  • Stop smoking
  • Nicotine replacement therapy
Pharmacological
  • NAC
  • Steroid if inflammatory
  • Antifibrotic agent like pirfenidone
Surgical
  • Single lung transplant

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